Is dermatofibrosarcoma protuberans inherited?

Is dermatofibrosarcoma protuberans inherited?

Dermatofibrosarcoma protuberans results from a new mutation that occurs in the body’s cells after conception and is found only in the tumor cells. This type of genetic change is called a somatic mutation and is generally not inherited.

Is dermatofibrosarcoma protuberans malignant?

Dermatofibrosarcoma protuberans (DFSP) is a rare dermal malignancy affecting the deep dermis and subcutaneous tissues. It was first reported by Darier and Ferrand in 1924. This tumor is locally aggressive with high recurrence rates, but rarely metastasizes.

Do dermatofibromas keep growing?

Dermatofibromas tend to grow slowly. The growths typically have some defining characteristics that can help identify them.

Can a Dermatofibroma get bigger?

Dermatofibromas are usually painless, but some people experience tenderness or itching. Most often, a single nodule develops, but some people can develop many dermatofibromas. They rarely grow larger than a half-inch in diameter.

What is the prognosis of dermatofibrosarcoma protuberans ( DFSP )?

Dermatofibrosarcoma Protuberans (DFSP) Prognosis. Dermatofibrosarcoma protuberans (DFSP) is a rare type of cancer in which a soft tissue sarcomatous tumor forms deep in the skin. It begins as a small flat lesion, rarely more than 5 cm across, with neither pain nor tenderness. It may be flesh-colored, but more often reddish or purple.

How does dermatofibrosarcoma protuberans look like?

Dermatofibrosarcoma protuberans is an uncommon cancer in which tumors arise in the deeper layers of skin. The tumor usually starts as a small, firm patch of skin; it may be purplish, reddish, or flesh-colored.

What are the options for treatment of dermatofibrosarcoma?

Treatment options may include: Surgery to remove the cancer. For most cancers, your doctor may recommend a procedure to remove the cancer and some of the healthy tissue that surrounds it (excisional surgery with a normal margin of tissue). This makes it more likely that all of the cancer cells are removed during surgery.

Where can I find dermatofibrosarcoma home reference?

DermNet NZ is an online resource about skin diseases developed by the New Zealand Dermatological Society Incorporated. DermNet NZ provides information about this condition. Genetics Home Reference (GHR) contains information on Dermatofibrosarcoma protuberans.